Overview |
bs-8719R-Cy5.5 |
LRP130 Polyclonal Antibody, Cy5.5 Conjugated |
WB, IF(IHC-P) |
Human, Mouse, Rat |
Specifications |
Cy5.5 |
Rabbit |
KLH conjugated synthetic peptide derived from human LRP130 |
165-270/1394 |
Polyclonal |
IgG |
1ug/ul |
Purified by Protein A. |
Aqueous buffered solution containing 0.01M TBS (pH 7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. |
Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles. |
Target |
LRPPRC; 130 kDa leucine-rich protein; GP130; Leucine-rich PPR-mot containing protein; LRP 130; LPPRC_HUMAN. |
Leucine-rich protein (LRP130) is a cytoplasmic mRNA-binding protein likely to be involved in the processing of mitochondrial DNA transcripts. Defects in the LRPPRC gene that encodes LRP130 result in the French-Canadian type of Leigh syndrome, a severe neurological disorder characterized by lesions in the subcortical region of the brain. LRP130 also interacts with the low-affinity receptor for leukemia inhibitory factor to produce an intracelluar signal cascade. |
Application Dilution |
WB |
1:300-5000 |
IF(IHC-P) |
1:50-200 |