Miglustat HCl
Overview | |
Catalog # | bs-82484c-5-mg |
Product Name | Miglustat HCl |
Specifications | |
Storage Buffer | white solid |
Storage Condition | -20°C |
Target | |
Product Information | Orally active ceramide-specific glycosyltransferase and α-glucosidase I and II inhibitor.1 Rescues trafficking-deficient F508del-CFTR in human airway epithelial cells via inhibition of ER α-glucosidases I and II.2 Pharmacological chaperone for glucocerebrosidase degradation.3 Clinically useful agent for Gaucher disease type 1.4 Stabilizes neurological disorders in Niemann-Pick disease type C.5 |
Description | CAS Number: 210110-90-0 Chemical Name: N-Butyldeoxynojirimycin HCl Molecular weight: 255.74 Formula: C10H21NO4 HCl Solubility: DMSO (20 mg/ml) Water (20 mg/ml) Physical Properties: White solid Purity: 98% by TLC, NMR (Conforms) |