Overview |
bsm-54753R |
LMAN1 Monoclonal Antibody |
WB, IHC-P |
Human, Mouse, Rat |
Specifications |
Unconjugated |
Rabbit |
Synthetic peptide within N-terminal Human LMAN1. |
Monoclonal |
1H9 |
IgG |
1ug/ul |
Purified by Protein A. |
Aqueous buffered solution containing 1xTBS (pH7.4), 1%BSA, 40%Glycerol and 0.05% Sodium Azide. |
Store at -20°C for 12 months. |
Target |
3998 |
P49257 |
Endoplasmic reticulum membrane, Golgi apparatus membrane, ER-Golgi intermediate compartment membrane |
Endoplasmic reticulum golgi intermediate compartment protein 53 antibody, ER-Golgi intermediate compartment 53 kDa protein antibody, ERGIC-53 antibody, ERGIC53 antibody, ERGIC53 like protein antibody, F5F8D antibody, FMFD1 antibody, Gp58 antibody, Intracellular mannose specific lectin antibody, Intracellular mannose-specific lectin MR60 antibody, Lectin mannose binding 1 antibody, Lectin mannose-binding 1 antibody, Lman1 antibody, LMAN1 like protein antibody, LMAN1_HUMAN antibody, MCFD1 antibody, MR60 antibody, Protein ERGIC-53 antibody |
The protein encoded by this gene is a type I integral membrane protein localized in the intermediate region between the endoplasmic reticulum and the Golgi, presumably recycling between the two compartments. The protein is a mannose-specific lectin and is a member of a novel family of plant lectin homologs in the secretory pathway of animal cells. Mutations in the gene are associated with a coagulation defect. Using positional cloning, the gene was identified as the disease gene leading to combined factor V-factor VIII deficiency, a rare, autosomal recessive disorder in which both coagulation factors V and VIII are diminished. [provided by RefSeq, Jul 2008] |
Application Dilution |
WB |
1:300-5000 |
IHC-P |
1:200-400 |