Miglustat HCl

Overview
Catalog #	bs-82484c-5-mg
Product Name	Miglustat HCl
Specifications
Storage Buffer	white solid
Storage Condition	-20°C
Target
Product Information	Orally active ceramide-specific glycosyltransferase and α-glucosidase I and II inhibitor.1 Rescues trafficking-deficient F508del-CFTR in human airway epithelial cells via inhibition of ER α-glucosidases I and II.2 Pharmacological chaperone for glucocerebrosidase degradation.3 Clinically useful agent for Gaucher disease type 1.4 Stabilizes neurological disorders in Niemann-Pick disease type C.5
Description	CAS Number: 210110-90-0 Chemical Name: N-Butyldeoxynojirimycin HCl Molecular weight: 255.74 Formula: C10H21NO4 HCl Solubility: DMSO (20 mg/ml) Water (20 mg/ml) Physical Properties: White solid Purity: 98% by TLC, NMR (Conforms)