Miglustat HCl (N-Butyldeoxynojirimycin)
| Overview | |
| Catalog # | bs-80506C |
| Product Name | Miglustat HCl (N-Butyldeoxynojirimycin) |
| Specifications | |
| Storage Buffer | powder |
| Storage Condition | -20°C |
| Target | |
| Product Information | Molecular Weight:255.74 Formula:C10H21NO4 HCl Purity:>98% Solubility:Soluble in DMSO (up to 20 mg/ml) or in Water (up to 20 mg/ml). Chemical Name:N-Butyldeoxynojirimycin HCl |
| Description | Orally active ceramide-specific glycosyltransferase and α-glucosidase I and II inhibitor.1 Rescues trafficking-deficient F508del-CFTR in human airway epithelial cells via inhibition of ER α-glucosidases I and II.2 Pharmacological chaperone for glucocerebrosidase degradation.3 Clinically useful agent for Gaucher disease type 1.4 Stabilizes neurological disorders in Niemann-Pick disease type C.5 |
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